Xeroderma pigmentosum and its treatment













These horrifying pictures are of facial tumors suffered by patients of Xeroderma pigmentosum.This is a genetic condition in which body ability to repair genetic damage is greatly impaired. As a result theses children are greatly susceptible to damaging effects of UV rays. They develop facial skin tumors  or in other exposed part of body.

This patient had these skin tumors which were excised and skin grafted. Bilateral neck dissection was done as it showed enlarged lymph nodes. Patient tolerated surgery as were happy to get rid of horrendous deformity it was causing. All margins were negative and nodes were negative.


Dr Adhishwar  Sharma
MBB,BS MS Gen Surgery PGIMER Chd
Mch Plastic Surgery
brahmanandclinic.com
8860650846, adhishwar7@gmail.com

































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